Pulmonary stenosis

The majority of pulmonary stenosis are conginetal. It cause by abnormal formation of the pulmonary valve leaflets during fetal cardiac development. Rarely, rheumatic heart disease, malignant carcinoid, or extrinsic compression by a tumor or sinus of valsalva aneurysm may lead to pulmonary stenosis.

Pulmonary stenosis can be valvular, subvalvular or supravalvular. Valvular pulmonary stenosis is the most common, accounting for 90% cases.

Subvalvular pulmonary stenosis can occur as part of a conginetal heart complex such as tetralogy of Fallot or as a result of hypertrophic obstructive cardiomyopathy involving the right side of the heart.

Patients with pulmonary stenosis may live for extended periods completely without symptoms and frequently survive past the age of 70 years without surgical intervention, when they do occur, include tachypnea, syncope, angina or hepatomegaly and peripheral edema.
Pulmonary stenosis